Background: Herlyn-Werner-Wunderlich (HWW) syndrome is a very rare congenital anomaly of the urogenital tract\r\ninvolving M�¼llerian ducts and Wolffian structures, and it is characterized by the triad of didelphys uterus,\r\nobstructed hemivagina and ipsilateral renal agenesis. It generally occurs at puberty and exhibits non-specific and\r\nvariable symptoms with acute or pelvic pain shortly following menarche, causing a delay in the diagnosis.\r\nMoreover, the diagnosis is complicated by the infrequency of this syndrome, because M�¼llerian duct anomalies\r\n(MDA) are infrequently encountered in a routine clinical setting.\r\nCases presentation: two cases of HWW syndrome in adolescents and a differential diagnosis for one case of a\r\ndifferent MDA, and the impact of magnetic resonance (MR) imaging technology to achieve the correct diagnosis.\r\nConclusions: MR imaging is a very suitable diagnostic tool in order to perform the correct diagnosis of HWW\r\nsyndrome.
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